Plexiform fibrohistiocytic tumor
Plexiform fibrohistiocytic tumor (PFHT) is a rare type of soft tissue tumor that typically occurs in children and young adults. It was first described in the medical literature in 1988. PFHT is considered a low-grade malignancy, meaning it has the potential to spread to other parts of the body, but this is uncommon.
Signs and Symptoms[edit | edit source]
Patients with PFHT typically present with a slow-growing, painless mass. The most common locations for these tumors are the upper extremities, followed by the head and neck region. However, they can occur anywhere in the body.
Diagnosis[edit | edit source]
The diagnosis of PFHT is made based on the findings of a biopsy of the tumor. The tumor is composed of a mixture of fibroblasts and histiocytes, arranged in a distinctive plexiform pattern. The cells are typically spindle-shaped and have a moderate amount of cytoplasm. There may also be areas of necrosis or hemorrhage within the tumor.
Treatment[edit | edit source]
The primary treatment for PFHT is surgical removal of the tumor. In some cases, chemotherapy or radiation therapy may be used as well.
Prognosis[edit | edit source]
The prognosis for patients with PFHT is generally good, with a high rate of long-term survival. However, the tumor can recur in up to one-third of cases, and metastasis can occur, although this is rare.
See Also[edit | edit source]
References[edit | edit source]
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