Non-cirrhotic portal fibrosis
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| Non-cirrhotic portal fibrosis | |
|---|---|
| Autosomal recessive - en.svg | |
| Non-cirrhotic portal fibrosis is inherited in an autosomal recessive manner
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Non-cirrhotic portal fibrosis (NCPF) is a chronic liver disease[1] and type of non-cirrhotic portal hypertension (NCPH).
Presentation[edit]
It is characterized by 'obliterative portovenopathy', which leads to various problems such as portal hypertension, massive splenomegaly, and variceal bleeding. It is estimated that about 85% of people with NCPF have repeated episodes of variceal bleeding.[2]
Diagnosis[edit]
Hallmark of the disease is thrombosis/sclerosis of branches of portal vein. Vessels formed are often termed as mesangiosinusoids or periportal cavernoma.
Treatment[edit]
![[icon]](/wiki/File:Wiki_letter_w_cropped.svg){kind=small} | This section is empty. You can help by adding to it. (September 2017) |
References[edit]
- ↑ "Non-cirrhotic portal fibrosis: one disease with many names? An analysis from morphological study of native explant livers with end stage chronic liver disease.".Journal of Clinical Pathology.July 2011;64(7)
- 592–8.doi:10.1136/jcp.2010.087395.PMID:21685145.
- ↑ "Non-cirrhotic portal fibrosis.".Journal of Gastroenterology and Hepatology.December 2002;17 Suppl 3
- S214-23.PMID:12472939.
External links[edit]
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